Date of Presentation:12/20/2021

Attending pathologist: Wei Chen, MD, PhD

Presented by: Saba Shafi, MD

Prepared by: Saba Shafi, MD

Organ:Small Intestine

HISTORY:

A 36-year-old male with no past medical history who initially presented with progressively worsening abdominal pain and distension. CT AP was demonstrative of a large mass within the central portion of the abdomen measuring 24.6 x 13.7 x 21.7 cm. This encased or was intimately associated with a mildly dilated loop of small bowel within the left lower quadrant measuring 3.9 cm in caliber. Concerning for malignancy including gastrointestinal stromal tumor, spindle cell neoplasm, and lymphoma.

GROSS:

What is the most likely diagnosis?

  1. Myofibromatosis
  2. Sclerosing mesenteritis/idiopathic retroperitoneal fibrosis
  3. Mesenteric desmoid-type fibromatosis
  4. Gastrointestinal stromal tumor (GIST)
Mesenteric desmoid-type fibromatosis